Pulmonary capillary hemangiomatosis. A rare cause of pulmonary hypertension. The first Brazilian case* HELANO NEIVA DE CASTRO1, MARA RÚBIA FERNANDES DE FIGUEIREDO1, NORMA SELMA SANTOS2, TERESA NEUMA ALBUQUERQUE GOMES NOGUEIRA3, MARIA DA PENHA UCHOA4,

Pulmonary capillary hemangiomatosis is a rare disorder characterized by a proliferation of capillaries that invade the pulmonary interstitium and alveolar septae. Herein, we report the first Brazilian case of pulmonary capillary hemangiomatosis. A 21-year-old man presented with severe pulmonary hypertension that eventually resulted in his death. Upon admission, a computed tomography scan of the chest revealed diffuse ill-defined bilateral pulmonary nodules. A postmortem lung biopsy revealed pronounced multifocal proliferation of capillaries in the alveolar walls, interlobular septa and peribronchial connective tissue. A diagnosis of pulmonary capillary hemangiomatosis should be considered in patients presenting pulmonary hypertension and suspicious changes on high-resolution computed